Hemophilia affects the process of joints: bleeding-inflammation-damage!

Hemophilic arthritis is a very serious problem. Improper treatment can lead to an increase in the teratogenic rate of hemophilia patients! However, targeted and timely treatment can greatly avoid this situation. The effects of hemophilia arthropathy mostly occur in moderate to severe hemophilia patients with frequent bleeding. Generally manifested in joint hemorrhage, hematoma, mostly in the knee joint, ankle, hip, shoulder, elbow. &nbsp.&nbsp.&nbsp.The first process&nbsp.&nbsp. is the bleeding period, when the hemophilia’s joints suddenly and acutely bleed with severe pain, the joints are swollen, tender, and movement is restricted, and the joints begin to appear Protective stiffness, sometimes with fever and increased white blood cells, is usually misdiagnosed as septic arthritis. &nbsp.&nbsp.&nbsp.The second process&nbsp.&nbsp. is the period of inflammation. Hemophilia is caused by repeated bleeding in the joints, which leads to thickening of the joint capsule and synovium, followed by joint swelling, restricted movement, and friction or friction during exercise. Bone sound. For children, the hematoma after hemophilic intra-articular hemorrhage is generally absorbed slowly, and it takes about three to six weeks. &nbsp.&nbsp.&nbsp.The third process&nbsp.&nbsp. is the degeneration period. Hemophilia’s joint movement has been severely impaired, muscle atrophy and other symptoms. The knee joint is prone to hyperplasia, flexion, contracture and other deformities, and then serious and easy to cause Disabled. &nbsp.&nbsp. In addition to joint disease, hemophilic arthritis can cause hemophilic cysts due to bleeding under the fascia, subperiosteal, or muscle. X-rays can be used to check the severity of normal bone, bone cysts, osteoporosis, and joint damage at different stages of hemophilic arthritis. Take timely targeted treatment and perfect preventive measures!

[Knock on the blackboard] Worry about low platelets inducing intracranial hemorrhage, teach you how to observe!

Regarding simple immune thrombocytopenia, the main hazard risk is autocoagulation and bleeding. Especially for patients whose values ​​are too low (less than 20), it is clinically verified that there is a high risk of internal bleeding. For patients in this area, how to make protective observations? The relevant analysis is carried out below. [Knock on the blackboard] Worry about low platelets causing intracranial hemorrhage, teach you how to make observations! The first step (observe well) observe the symptoms of patients with thrombocytopenia. If the patient has severe headaches, vomiting, blurred vision, stiff neck, or even impaired consciousness, it means that the patient has intracranial hemorrhage. If the first step occurs in the second step In this case, it is necessary to give oxygen immediately, take the supine position, keep the airway unobstructed, and notify the physician to do all rescue work, and apply hemostatic drugs and drugs to reduce intracranial pressure as prescribed by the doctor. The third step is based on the current real-time situation, it is necessary to give an ice pack or ice cap to the head, and closely observe the changes in blood pressure, pulse, breathing, pupils and consciousness. Observe the changes in the patient’s consciousness and pupils after the application of dehydrating drugs, observe for signs of bleeding in other important organs, and monitor platelet counts. (More knowledge comes from the bottom right of the picture) The fourth step is to be comforted if the thrombocytopenia patients are overly irritable, because irritable mood swings will aggravate brain hemorrhage. At the stage of medical treatment, appropriate sedatives should be given according to the doctor’s advice, and attention should be paid to avoid excessive sedation, so as not to affect the observation of the condition, and at the same time, add bed guards to prevent falling from bed. In summary, for patients with a value lower than 20, especially single patients, special attention should be paid! Timely detection of early manifestations of internal bleeding of thrombocytopenia can prevent the risk of related complications in time. In the final analysis, only by restoring the platelet value to the normal range as soon as possible can the risk of internal bleeding be avoided. Learn more about “disease knowledge” or “thrombocytopenia patient group communication” and other WeChat search public number: xxbjs

Hemophilia: What should a comprehensive medical team do?

Many patients with severe hemophilia have been diagnosed since they were young, and they will inevitably encounter a series of problems during their growth. The prevention and treatment measures carried out by a comprehensive medical team are very important! Standard medical team-“Thoughtful” prevention and treatment measures for all aspects of hemophilia [Complete treatment] It has a full range of drug therapies for the treatment of hemophilia, and controls the activity, purification, purity calculation of various therapeutic drugs, etc.; [Professional evaluation] evaluates blood Prevention and treatment of the risk of joint bleeding and internal bleeding in patients with friendly diseases, and rehabilitation treatment; combined with imaging physicians to assess the progress of bone and joint disease in patients with hemophilia, reduce the rate of teratogenicity and disability in patients with severe and frequent intra-articular hemorrhage; [Psychological counseling] Pay attention to the psychological development of patients with hemophilia and the psychological changes in the growth of children; [Oral care] For the group of children with hemophilia, professional dentists pay attention to the children’s teeth replacement, tooth extraction, etc. and popularize relevant precautions ; [Genetic counseling] Provide genetic counseling and protection popularization for non-severe hemophilia groups, such as genetic carrier, acquired, mild von Willebrand disease, etc.; … face comprehensive diagnosis and treatment of hemophilia Medical model, refer to the above. I hope that such a comprehensive hemophilia diagnosis and treatment team can be popularized, so that more people can pay attention to hemophilia, and concentrate all resources to provide services for hemophilia in all aspects, so that patients can reduce or avoid joint disease and prevent disability, like Live like a normal person. Learn more about “disease knowledge” or “hemophilia group communication” and other WeChat search public number: xueyb120

Hemophilia group: There are three main processes for joint disease!

Hemophilic arthritis is a very serious problem. Improper treatment can lead to an increase in the teratogenic rate of hemophilia patients! However, targeted and timely treatment can greatly avoid this situation. Doctors said that the effects of hemophilia arthropathy mostly occur in patients with moderate to severe hemophilia who have frequent bleeding. Generally manifested in joint hemorrhage, hematoma, mostly in the knee joint, ankle, hip, shoulder, elbow. [Not to be ignored] The process of hemophilia affecting joints: bleeding-inflammation-damage! The first process is the bleeding period. Sudden and acute bleeding in the joints of hemophilia is accompanied by severe pain. There is obvious swelling in the joints, obvious tenderness, and limited movement. The joints begin to appear in a state of protective stiffness, sometimes with fever, Phenomenon such as increased white blood cells, so it is generally easy to be misdiagnosed as septic arthritis. The second process is the period of inflammation. Hemophilia is caused by repeated bleeding in the joints, which results in thickening of the joint capsule and synovium, followed by joint swelling, restricted movement, and friction or bone noise during exercise. For children, the hematoma after hemophilic intra-articular hemorrhage is generally absorbed slowly, and it takes about three to six weeks. The third process is the degeneration period. Hemophilia’s joint movement has been severely damaged, muscle atrophy and other symptoms, and the knee joint is prone to deformities such as hyperplasia, flexion, and contracture, and then severe and easily disabled. In addition to joint disease, hemophilic arthritis can cause bleeding in the subfascia, subperiosteal, or muscle to cause hemophilic cysts. X-rays can be used to check the severity of normal bone, bone cysts, osteoporosis, and joint damage at different stages of hemophilic arthritis. Take timely targeted treatment and perfect preventive measures! Learn more about “disease knowledge” or “hemophilia group communication” and other WeChat search public number: xueyb120