Hemophilia is currently not curable. It is a lifelong disease that can only be treated symptomatically, such as blood transfusion or blood transfusion factor. The key is to strengthen care and prevention in daily life to reduce and avoid causing bleeding. There are currently three types of hemophilia, namely hemophilia A, hemophilia B, and hemophilia C. Hemophilia A is due to the lack of blood clotting factor m, while hemophilia B and hemophilia C are lacking. Coagulation factor k and clotting factor knives, these types of hemophilia have certain genetic laws. Both hemophilia A and hemophilia B are sexually recessive. Common is hemophilia A, which is characterized by the onset of males in the family, while females are the carriers of the disease but do not develop the disease. The other two types of hemophilia are both male and female. Home care points Because the disease is a lifelong disease, it is often heavier at onset. Therefore, prevention and care within the family have extraordinary significance for the prognosis of patients and the quality of daily life. 1. Patients and relatives must have a full understanding of the disease, relatives should give patients enough care and love, patients themselves should establish self-confidence, self-reliance, self-improvement of life concepts, self-care, to minimize the incidence of disease and improve Quality of Life. 2. Prevention and care of bleeding (1) “Prevention and care of bleeding”, pay special attention to avoiding trauma, when going to the hospital, explain the condition to the doctor and nurse, and avoid intramuscular injection as much as possible. Do all kinds of safety precautions in the home, try to avoid the use of sharp objects, such as needles, scissors, knives, etc. (2) Normally, when there is no bleeding, proper exercise is beneficial to reduce the recurrence of the disease. However, when there is active bleeding, it is necessary to limit the activity to avoid aggravating the bleeding. (3) When the joint bleeds, you should lie on the bed, fix the limb with splint, put it in a functional position, restrict movement, and apply local cold compress and bandage with elastic bandage. After the joint bleeding stops and the swelling and pain disappear, appropriate joint activities can be performed to prevent deformities and stiffness caused by long-term joint fixation. 3. People who have anemia due to heavy bleeding should strengthen the care of anemia.
Hemophilia is currently not curable. It is a lifelong disease that can only be treated symptomatically, such as blood transfusion or blood coagulation factor transfusion. The key lies in strengthening care and prevention in daily life to reduce and avoid bleeding. There are currently three types of hemophilia, namely hemophilia A, hemophilia B, and hemophilia C. Hemophilia A is due to the lack of blood clotting factor m, while hemophilia B and hemophilia C are lacking. Coagulation factor k and clotting factor knives, these types of hemophilia have certain genetic laws. Both hemophilia A and hemophilia B are sexually recessive. The most common is hemophilia A, which is characterized by the onset of males in the family, while females are the carriers of the disease but do not develop the disease. The other two types of hemophilia are both male and female. The main point of home care is that the disease is a lifelong disease, and it is often heavier at onset. Therefore, prevention and care in the home have extraordinary significance for the prognosis of patients and the quality of daily life. 1. Patients and relatives must have a full understanding of the disease, relatives should give patients enough care and love, patients themselves should establish self-confidence, self-reliance, self-improvement of life concept, do self-care, minimize the incidence of disease and improve Quality of Life. 2. Prevention and Nursing of Bleeding (1) “Prevention and Nursing of Bleeding”, pay special attention to avoiding trauma, when going to the hospital, explain the condition to the doctor and nurse, and avoid intramuscular injection as much as possible. Do all kinds of safety precautions in the home, try to avoid the use of sharp objects, such as needles, scissors, knives, etc. (2) In the absence of bleeding, proper exercise is beneficial to reduce the recurrence of the disease. However, when there is active bleeding, it is necessary to limit the activity to avoid aggravating the bleeding. (3) When the joint bleeds, you should stay in bed, fix the limbs with splints, put them in a functional position, restrict movement, and apply local cold compress and bandage with elastic bandage. After the joint bleeding stops and the swelling and pain disappear, appropriate joint activities can be performed to prevent deformities and stiffness caused by long-term joint fixation. 3. People who have anemia due to heavy bleeding need to strengthen anemia care
At present, there are still some patients who are difficult to obtain appropriate supplemental coagulation factor therapy (thick coagulation factor preparation, fresh plasma, cryoprecipitate). In this regard, appropriate conservative treatment can be used in time to reduce bleeding or hemostasis, and prevent bleeding from damaging the body. Without coagulation factors, there are three points for conservative treatment of hemophilia ①: posture ②: ice compress ③: lying on the upper body of the bleeding site, such as the waist and elbows, this should use the sling of the support plate. If there is cryoprecipitate or fresh plasma, this should be entered in one unit when the bleeding is found, and then lost in 24 hours. If the patient is suffering from pain, an analgesic can be used, but aspirin should be avoided. When the pain, stiffness, and limited range of motion caused by joint bleeding are alleviated, it is important to start exercising the muscle groups around the joint immediately. Strong muscle groups around joints can prevent repeated bleeding and chronic arthritis. Joint flexion and extension training can also be performed without input of hemostatic drugs. In the same way, the bleeding in the elbow should be done gently. The use of high-top shoes or tennis shoes is helpful to prevent repeated ankle bleeding, especially for toddlers and children. Remarks on other bleeding related notes. Recently, patients have mentioned throat and nasal pain and pectoralis major and calf bleeding problems: throat and nasal pain: the tonsils are usually the largest and often accompanied by inflammation. Inflamed tonsils can cause severe bleeding. Similarly, severe coughing can also cause bleeding. Antibiotics can be used, and the diet should be cold fluid until recovery. If it is necessary to have an antitussive, antitussive medicine with a substitute for it is very effective. Bleeding at the abdominal muscles: A large amount of bleeding can be stored in the space of the pectoralis major, back muscles and peritoneum, and can cause anemia or even shock. Patients with unexplained paleness, weak drowsiness, and pain in the lower abdomen need to consider this aspect and seek medical attention. In addition, bleeding in these parts, such as the lower leg, is very dangerous because blood presses nerves and blood vessels and must lie still until the hematoma subsides. If you have any questions about this article or the disease, please feel free to follow us on WeChat and find out more: xueyb120
Assistant Hu Guisheng WeChat: dd326751 When some children are playing wantonly, some children should always pay attention to it, fearing that they will bump into them-accidental injuries in life may cause blood flow to stop, and the body is like glass “. They are hemophiliacs and are therefore called “glass people”. & nbsp. Hemophilia is a bleeding disorder with inherited blood coagulation dysfunction. Hemophilia mainly manifests as traumatic or spontaneous bleeding of joints and muscles. & nbsp. Experts emphasize that childhood is a critical period for the treatment of hemophilia, and standardized preventive treatment should be taken as early as possible. Early intervention is beneficial to the development of children’s joints, reduces bleeding symptoms, and reduces the rate of disability. & nbsp. There are two main types of hemophilia. & hemophilia A: lack of active factor VIII (8); hemophilia B: lack of active factor IX (9). Among all hemophilia patients, hemophilia A patients account for 80% to 85%, and hemophilia B patients account for 15% to 20%. An early national survey showed that the prevalence of hemophilia in China is 2.73 per 100,000. & nbsp. Clinical studies have shown that among children under 12 years of age who receive Immexizumab once a week for 58 weeks of preventive treatment, the annualized bleeding rate is only 0.3%, and the zero treatment bleeding rate is 77%. & nbsp. Regardless of the age of the patient and the presence of antibodies in the body, as the treatment time continues to increase, the patient’s treatment effect will be significantly improved, which can make more than 99% of the target joints stop frequent bleeding and avoid the occurrence of joint diseases and disabilities. However, due to the relatively insufficient social cognition of hemophilia, the low availability of drugs, and the existing treatment methods have certain limitations. & nbsp. Therefore, active preventive treatment can reduce the disability of joints in hemophiliacs and improve the quality of life. Preventive treatment is through regular, routine and continuous preventive infusion of coagulation factors to maintain the level of coagulation factors in the patient for more than 1% for a long time to ensure that the patient is close to the healthy level of normal people and maintain the normal function of joint muscles. Preventive treatment is recommended to start after the first joint bleeding or severe muscle bleeding.
Ts: There must be some special substances in the blood, which can automatically “close” the rupture of the blood vessel when bleeding. It can be known by turning on human physiology that these special substances are called coagulation factors. There are 13 kinds of clotting factors like “straight flush” in playing cards. Platelet factor and calcium ions are two of the “straight flush”. When the blood vessel ruptures and blood flows out, the platelets in it will release the coagulation factor. With the participation of plasma calcium ions, the coagulation factor will be activated in turn and eventually form fibrin. Numerous fibrin forms a very dense net on the bleeding wound, but it is very dense, blocking a large number of blood cells, forming a microscopic dyke visible to the naked eye-blood clot, blocking the turbulent blood flow. The “straight flush” in playing cards has different sizes, but the coagulation factor is not large or small, and the role is very important. If any one is missing, the bleeding will continue after the injury. For example, there is a genetic disease called hemophilia. This patient’s blood is naturally lacking in coagulation factors Ⅷ, Ⅸ, and X, which are called hemophilia A, B, and C, respectively. Once the patient is bleeding, it is difficult to stop the bleeding, so they are very afraid of the bleeding, let alone surgery. It can be seen that coagulation factors are very important to our body. Without them, the damage caused by brushing our teeth may also cause us to drain the last drop of blood. When hemorrhagic patients are encountered, hemostatic drugs are used to help hemostasis of coagulation factors from various links. Like hemostasis, it can also increase the number of platelets and encourage them to release coagulation factors, so that they are more tightly together with blood cells. Form clumps, blocking blood vessel rips. In the case of cerebral thrombosis and other diseases with enhanced blood coagulation, doctors try to prevent blood coagulation and increase the function of the fibrinolysis system, like heparin, which prevents the activation of thrombin and prevents fibrin from weaving into a net. It also prevents platelets from releasing blood coagulation factor. Urokinase and streptokinase can promote the function of fibrinolysis system, making it difficult to form thrombus, and dissolve the formed thrombus. WeChat search Yisuo will pay attention to the patient will know more: xueyb120
Whether it is for children or adults, you need to observe the performance caused by muscle and joint hematoma, which can occur after bleeding, you need to judge the degree and combine medical treatment to deal with it! For patients with hemophilia, in addition to regular review, blood pressure, pulse, etc. need to be supplemented. Specific related issues, related analysis below! [Nursing] What should be paid attention to hemomas of hemophilia? For family escorts, it is also necessary to observe the patient for signs of hematemesis, hemoptysis and other visceral bleeding! This is important! In addition, the performance of intracranial hemorrhage should also be noted. If you have headaches, vomiting, asymmetric pupils, or even unexplained coma, you need to report to a doctor in time and cooperate with emergency treatment (especially for coagulation factor levels less than 1% Of severe hemophiliacs)! The drugs used for hemophilia are mostly coagulation products, including coagulation factors, cryoprecipitates, etc. This is a conventional medication. The main effect is to increase the content of coagulation factors in hemophilia patients in a short period of time, which helps to promote blood coagulation. In terms of medication care, that is, infusion of coagulation factors, it should be infused immediately after retrieval. When using the cold precipitate, it should be melted in warm water at 37 ° C for 10 minutes and input as soon as possible! Patients with hemophilia need to pay attention to whether there is a transfusion reaction during the administration of infusion. Do not use medication indiscriminately as directed by your doctor to prevent increased bleeding. In addition, the coagulation factor is not a panacea. It only improves the therapeutic effect of its own coagulation factor in a short period of time, and it should not be randomly and inappropriately infused frequently. This may cause drug resistance problems with high probability. Hemophilia joint cavity care problems Joint care of hemophilia patients is very important, because hemophilia patients with lower blood coagulation factor levels are more likely to have bleeding performance in the joints, and improper treatment of joint bleeding many times may lead to hemophilia The patient has deformed joints and disability. Instructed to emphasize joint care! When hemorrhagic patients have hemorrhage in the joint cavity and the joint cannot move normally, they should brake locally and keep the limb in functional position. Do not load the affected limb until the swelling has completely resolved and muscle strength has not recovered. After the joint cavity bleeding is controlled, the family or medical staff needs to help the patient to carry out active or passive joint activities. The purpose of universal functional exercise is to prevent joint contracture, stiffness, muscle atrophy, and loss of function. When necessary, work out an activity plan with the patient to make it active. In addition, regarding psychological care is also very important, a good attitude can help promote the recovery of the condition. Every patient with hemophilia should have their own subjective consciousness to understand the main pathology of the disease and related basic protective measures, and encourage hemophiliacs to build confidence in defeating the disease. Ps: There are also new drugs entering the eyes of patients one after another, which has greatly improved in terms of prolonging the administration time and improving the efficacy. The curative problem of hemophilia is totally worth looking forward to! WeChat search Yisuo will pay attention to the patient will know more: xueyb120